Abnormal thoracoabdominal VISCERA arrangement (visceral heterotaxy) or malformation that involves additional CONGENITAL HEART DEFECTS (e.g., heart isomerism; DEXTROCARDIA) and/or abnormal SPLEEN (e.g., asplenia and polysplenia). Irregularities with the central nervous system, the skeleton and urinary tract are often associated with the syndrome.

Descriptor ID	D059446
MeSH Number(s)	C14.240.400.592 C14.280.400.592 C15.604.744.146 C16.131.077.401 C16.131.240.400.592
Concept/Terms	Heterotaxy Syndrome Heterotaxy Syndrome Heterotaxy Syndromes Syndrome, Heterotaxy Syndromes, Heterotaxy Visceral Heterotaxy Visceral Heterotaxy Heterotaxies, Visceral Heterotaxy, Visceral Visceral Heterotaxies Situs Ambiguus Viscerum Ambiguus Viscerum, Situs Ambiguus Viscerums, Situs Situs Ambiguus Viscerums Viscerum, Situs Ambiguus Viscerums, Situs Ambiguus Situs Ambiguus Ambiguus, Situs Polysplenia Syndrome Polysplenia Syndrome Polysplenia Syndromes Syndrome, Polysplenia Syndromes, Polysplenia Situs Ambiguus with Polysplenia Left Atrial Isomerism with Polysplenia Right Atrial Isomerism Right Atrial Isomerism Atrial Isomerism, Right Atrial Isomerisms, Right Isomerism, Right Atrial Isomerisms, Right Atrial Right Atrial Isomerisms Asplenia Syndrome Asplenia Syndrome Asplenia Syndromes Syndrome, Asplenia Syndromes, Asplenia Situs Ambiguus with Asplenia Right Atrial Isomerism with Asplenia Asplenia with Cardiovascular Anomalies Ivemark Syndrome Syndrome, Ivemark Left Atrial Isomerism Left Atrial Isomerism Atrial Isomerism, Left Atrial Isomerisms, Left Isomerism, Left Atrial Isomerisms, Left Atrial Left Atrial Isomerisms

Below are MeSH descriptors whose meaning is more general than "Heterotaxy Syndrome".

Below are MeSH descriptors whose meaning is related to "Heterotaxy Syndrome".

Below are MeSH descriptors whose meaning is more specific than "Heterotaxy Syndrome".